Mucinous Tubular and Spindle Cell Renal Cell Carcinoma (MTSC-RCC) with an Unusual Presentation in a Child

Main Article Content

Kanika Sharma
Anjan Dhua
Sandeep Agarwala
Seema Kaushal

Keywords

children, mucinous tubular and spindle cell carcinoma, renal cell carcinoma

Abstract

Mucinous tubular and spindle cell renal cell carcinoma (MTSC-RCC) is a rare but favorable variant of renal cell carcinoma, predominantly found in adults. Complete surgical excision is the treatment of choice. We are reporting an intriguing case of bilateral MTSC-RCC in a 13-year-old-boy with rapid disease progression, leading to metastatic disease and subsequent demise of the child.

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